颞下颌关节色素沉着绒毛结节性滑膜炎伴颅内扩展：病例系列及系统评价
Pigmented villonodular synovitis of the temporomandibular joint with intracranial extension: A case series and systematic review.
作者信息
Safaee Michael, Oh Taemin, Sun Matthew Z, Parsa Andrew T, McDermott Michael W, El-Sayed Ivan H, Bloch Orin
机构信息
Department of Neurological Surgery, University of California - San Francisco, San Francisco, California.
Department of Neurological Surgery, Northwestern University, Feinberg School of Medicine, Chicago, Illinois.
出版信息
Head Neck. 2015 Aug;37(8):1213-24. doi: 10.1002/hed.23717. Epub 2014 Jul 11.
BACKGROUND
Pigmented villonodular synovitis (PVNS) is a rare proliferative disorder of the synovial membrane. PVNS generally affects large joints but occasionally involves the temporomandibular joint (TMJ), with occasional extension into the middle cranial fossa. The purpose of this study was to report our experience with PVNS along with a focused literature review.
METHODS
Patients with PVNS of the TMJ treated at the University of California - San Francisco from 2007 to 2013 were reviewed. A PubMed search was performed to identify additional cases.
RESULTS
Five patients underwent surgical resection, with 1 recurrence at 61 months. A literature review identified 58 patients, 19 of which had intracranial involvement. Interestingly, intracranial extension was more common in men. Intracranial extension was not associated with an increased rate of recurrence.
CONCLUSION
PVNS of the TMJ is a rare entity associated with excellent outcomes, even with intracranial extension. Management should consist of maximal resection, with radiotherapy reserved for extensive or recurrent lesions.
背景
色素沉着绒毛结节性滑膜炎（PVNS）是一种罕见的滑膜增殖性疾病。PVNS通常累及大关节，但偶尔也会累及颞下颌关节（TMJ），并偶尔延伸至中颅窝。本研究的目的是报告我们治疗PVNS的经验并进行重点文献综述。
方法
回顾了2007年至2013年在加利福尼亚大学旧金山分校接受治疗的TMJ-PVNS患者。通过PubMed检索以确定更多病例。
结果
5例患者接受了手术切除，其中1例在61个月时复发。文献综述确定了58例患者，其中19例有颅内受累。有趣的是，颅内延伸在男性中更常见。颅内延伸与复发率增加无关。
结论
TMJ-PVNS是一种罕见的疾病，即使有颅内延伸，预后也很好。治疗应包括最大限度的切除，放疗仅用于广泛或复发性病变。
Zotero 插件