Luis-Miranda Raúl San, Arias-Mon-roy Laura G, Alcantar-Mendoza Mario Alberto, Cabrera-Arroyo Carlos, Mendoza-Reyes Edgar, Jarero Silvia Córdova
Ginecol Obstet Mex. 2014 Feb;82(2):93-104.
Fetal echocardiography is possible to confirm with great certainty the diagnosis, in utero, Ebstein's anomaly, as well as determine its perinatal prognosis.
Review the experience of 16 cases diagnosed with Ebstein's anomaly, using fetal echocardiography, analyzing "forecast echocardiographic parameters" set by Pavlova, Huhta and Barre.
retrospective and descriptive analysis. We analysed echocardiographic parameters and its correlation with the perinatal development of 16 cases diagnosed with Ebstein's anomaly.
Maternal age of our patients was 27.94 +/- 5.7 years, gestational age 31.3 +/- 3.6.) Mortality: in-utero 37.5% (n = 6), neonatal 50% (n = 8), survived 12.5% (n = 2). Cardiothoracic index 0.61 +/- 0.074, relationship foramen oval/heart atrial 0.6 +/- 0.015; obstruction to the way out of the right ventricle in 14 cases (87.5%). The deceased 81% presented degree of valvular displacement > 2.5; relationship RV/LV 2.24 +/- 0.37).
Cardiothoracic index fetal stage > 0.55, relationship oval foramen/interatrial septum < 0.3, obstruction to the way out and a degree of valvular displacement > 2.5, absence of back flow in arteriosus ductus and a ratio RV/LV > 2 are poor prognostic factors for Ebstein's anomaly.
胎儿超声心动图能够非常确切地在子宫内确诊埃布斯坦畸形，并确定其围产期预后。
回顾16例经胎儿超声心动图诊断为埃布斯坦畸形的病例经验，分析帕夫洛娃、胡塔和巴雷设定的“超声心动图预测参数”。
回顾性和描述性分析。我们分析了16例经诊断为埃布斯坦畸形病例的超声心动图参数及其与围产期发育的相关性。
我们患者的母亲年龄为27.94±5.7岁，孕周为31.3±3.6周。死亡率：宫内37.5%（n = 6），新生儿50%（n = 8），存活12.5%（n = 2）。心胸指数0.61±0.074，卵圆孔/心房关系0.6±0.015；14例（87.5%）右心室流出道梗阻。死亡者中81%瓣膜移位程度>2.5；右心室/左心室关系2.24±0.37。
胎儿期心胸指数>0.55、卵圆孔/房间隔关系<0.3、流出道梗阻、瓣膜移位程度>2.5、动脉导管无反流以及右心室/左心室比值>2是埃布斯坦畸形的不良预后因素。
