Department of Cardiothoracic Transplantation and Mechanical Support, Royal Brompton and Harefield NHS Trust, London, United Kingdom.
Department of Cardiothoracic Transplantation and Mechanical Support, Royal Brompton and Harefield NHS Trust, London, United Kingdom.
Ann Thorac Surg. 2014 May;97(5):1804-6. doi: 10.1016/j.athoracsur.2013.07.132.
We describe the case of a 29-year-old woman with end-stage chronic obstructive pulmonary disease secondary to vascular Ehlers-Danlos syndrome. Because of critical deterioration, respiratory arrest, and complete lung failure, she required urgent implantation of a venovenous extracorporeal membrane oxygenator as a bridge to lung transplantation. After 6 days of extracorporeal life support, a successful bilateral sequential lung transplantation was performed. This is the first case of lung transplantation in a patient with a diagnosis of chronic obstructive pulmonary disease secondary to Ehlers-Danlos syndrome.
我们描述了一例 29 岁女性终末期慢性阻塞性肺疾病继发于血管型埃勒斯-当洛斯综合征。由于病情急剧恶化、呼吸停止和完全性肺衰竭，她需要紧急植入静脉-静脉体外膜肺氧合机作为肺移植的桥梁。在体外生命支持 6 天后，成功地进行了双侧序贯式肺移植。这是首例诊断为慢性阻塞性肺疾病继发于埃勒斯-当洛斯综合征的患者进行肺移植。
