Patel Ramnik V, Johal Navroop, Evans Kathryn, Mushtaq Imran
Department of Paediatric Urology, University College London Hospitals NHS Foundation Trust, London, UK Department of Paediatric Urology, Great Ormond Street Children Hospital NHS Trust, London, UK.
Department of Paediatric Urology, Great Ormond Street Children Hospital NHS Trust, London, UK.
BMJ Case Rep. 2014 May 15;2014:bcr2013202967. doi: 10.1136/bcr-2013-202967.
We report a 7-year-old boy who had antenatally diagnosed and postnatally confirmed asymptomatic right congenital hydronephrosis secondary to ureteropelvic junction obstruction with the anteroposterior diameter ranging from 7 to 15 mm on serial ultrasound scans till the age of 6 years. He then presented with recurrent attacks of Dietl's crisis almost every month in the seventh year of his life and eluded diagnosis for over a year at various national hospitals, and ended up with an international referral to us. Investigations of the acute attacks clinched the diagnosis of ureteral polyp causing intermittent crisis and he underwent segmental resection and reconstruction in the form of dismembered Anderson-Hyne pyeloplasty with good recovery. Our case revealed that prenatally detected hydronephrosis may worsen after spontaneous postnatal improvement and a polyp acting as a flip valve may produce intermittent hydronephrosis and symptoms later in life. The child should undergo urgent investigations during acute symptoms.
我们报告了一名7岁男孩,其先天性右侧肾盂积水在产前被诊断出,产后经确认,该积水由输尿管肾盂连接处梗阻引起,且无症状。在6岁之前的系列超声扫描中,肾盂前后径为7至15毫米。在其7岁时,几乎每月都会出现迪特尔危象(Dietl's crisis)的反复发作,在国内多家医院未能确诊长达一年多,最终被转诊至我院。对急性发作的检查确诊为输尿管息肉导致间歇性危象,他接受了节段性切除,并采用安德森-海恩(Anderson-Hyne)离断式肾盂成形术进行重建,恢复良好。我们的病例显示,产前检测到的肾盂积水在出生后自发改善后可能会恶化,息肉作为一个翻转瓣膜可能会在以后的生活中产生间歇性肾盂积水和症状。在出现急性症状时,患儿应接受紧急检查。