原发性心脏滑膜肉瘤。一种预后较差的罕见肿瘤。

Primary cardiac synovial sarcoma. A rare tumor with poor prognosis.

作者信息

Khan Habib, Chaubey Sanjay, Edlin Joy, Wendler Olaf

机构信息

Department of Cardiothoracic Surgery, Kings College Hospital/King's Health Partners, London, UK

Department of Cardiothoracic Surgery, Kings College Hospital/King's Health Partners, London, UK.

出版信息

Asian Cardiovasc Thorac Ann. 2014 Sep;22(7):835-8. doi: 10.1177/0218492313483584. Epub 2013 Oct 8.

DOI:10.1177/0218492313483584

PMID:24887816

Abstract

Synovial sarcoma comprises approximately 10% of all soft tissue tumors. Primary cardiac synovial sarcoma is exceedingly rare and accounts for<1% of all primary cardiac tumors. These tumors are highly aggressive with survival<1 year, even with surgery, chemotherapy, or radiation. We describe the case of a 45-year-old gentleman with primary cardiac synovial sarcoma of the heart, metastasizing to the lung. The tumor was resected, and the patient underwent chemotherapy with regression of the lung nodules.

摘要

滑膜肉瘤约占所有软组织肿瘤的10%。原发性心脏滑膜肉瘤极为罕见，占所有原发性心脏肿瘤的比例不到1%。这些肿瘤具有高度侵袭性，即使接受手术、化疗或放疗，生存期也不足1年。我们描述了一例45岁男性原发性心脏滑膜肉瘤转移至肺部的病例。肿瘤被切除，患者接受化疗后肺结节消退。