Kachanov Denis, Teleshova Margarita, Kim Eduard, Dobrenkov Konstantin, Moiseenko Roman, Usychkina Anastasya, Filin Andrey, Semenkov Alexey, Mitrofanova Anna, Konovalov Dmitry, Shamanskaya Tatyana, Novichkova Galina, Varfolomeeva Svetlana
Department of Clinical Oncology, Federal Scientific and Clinical Center of Pediatric Hematology, Oncology and Immunology named after Dmitry Rogachev, Moscow, Russian Federation.
Department of Clinical Oncology, Federal Scientific and Clinical Center of Pediatric Hematology, Oncology and Immunology named after Dmitry Rogachev, Moscow, Russian Federation.
Cancer Genet. 2014 Sep;207(9):412-4. doi: 10.1016/j.cancergen.2014.04.006. Epub 2014 Apr 21.
Malignant rhabdoid tumor (MRT) of the liver is a rare, highly aggressive tumor of early childhood. We report a 6-month-old boy who was diagnosed with MRT of the liver and presented with spontaneous tumor rupture. The patient underwent intensified chemotherapy and a radical surgical procedure. Twenty four months from the time of the diagnosis, he is alive without evidence of disease. This is the second report of prolonged survival after initial rupture of hepatic MRT.
肝脏恶性横纹肌样瘤(MRT)是一种罕见的、具有高度侵袭性的儿童早期肿瘤。我们报告一名6个月大的男孩,他被诊断为肝脏MRT并出现自发性肿瘤破裂。该患者接受了强化化疗和根治性手术。自诊断之时起24个月,他仍存活且无疾病迹象。这是关于肝脏MRT初次破裂后长期存活的第二篇报道。