Ahmed Bilal
Department of Prosthodontics and Oral Implantology, University Medical and Dental College, The University of Faisalabad, Faisalabad.
J Coll Physicians Surg Pak. 2014 May;24 Suppl 2:S132-4.
Papillon Lefevre Syndrome (PLS) is an autosomal recessive (AR) disorder affecting the skin and intra oral soft tissues resulting in palmo plantar hyperkeratosis with premature periodontal problems leading to early tooth loss and associated functional and psychological disturbances. This report presents management of a 17 years old girl suffering from PLS. She was presented with the chief complaint of loss of many permanent teeth and mobility of the remaining teeth. Most of the teeth were lost very early after their eruption due to swollen infected gums. There were no other associated problems except for the mild burning sensation of the palms and soles. A decision was made and remaining teeth were extracted in order to prevent aggressive bone loss. She was then managed using removable complete dentures with bilateral balanced occlusion. The patient is comfortable and functioning well with her new dentition.
帕皮永 - 勒费弗尔综合征（PLS）是一种常染色体隐性（AR）疾病，会影响皮肤和口腔内软组织，导致掌跖角化过度，并伴有过早出现的牙周问题，进而导致早期牙齿脱落以及相关的功能和心理障碍。本报告介绍了一名患有PLS的17岁女孩的治疗情况。她的主要诉求是多颗恒牙缺失以及剩余牙齿松动。大多数牙齿在萌出后不久就因牙龈肿胀感染而脱落。除了手掌和脚底有轻微烧灼感外，没有其他相关问题。做出了拔牙的决定，以防止严重的骨质流失。然后为她安装了具有双侧平衡咬合的可摘全口义齿进行治疗。患者佩戴新假牙后感觉舒适，功能良好。
