Tevlin R, Cahalane A M, Larkin J O, Treacy A, Connaghan D, Winter D C
Ir Med J. 2014 May;107(5):149-50.
We report a rare case of Erdheim-Chester Disease, a non-Langerhans cell histiocytosis. A 60-year old female presented with a seven-month history of vague abdominal symptoms. A large retroperitoneal mass was detected on computed tomography (CT), but multiple CT-guided biopsy samples were inconclusive. Laparoscopy revealed a mass in the distal ileum, which was resected. Histology and immuno-histochemistry supported a diagnosis of Erdheim-Chester Disease.
我们报告了一例罕见的 Erdheim-Chester 病,这是一种非朗格汉斯细胞组织细胞增多症。一名 60 岁女性出现了 7 个月的腹部模糊症状史。计算机断层扫描(CT)检测到一个巨大的腹膜后肿块,但多个 CT 引导下的活检样本结果不明确。腹腔镜检查发现回肠末端有一个肿块,遂将其切除。组织学和免疫组织化学检查支持 Erdheim-Chester 病的诊断。