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Seedless orchids: Issues in the anorchid adult.无籽兰花:无睾成年男性的问题
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2
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本文引用的文献

1
Clinical, biological and genetic analysis of anorchia in 26 boys.26 例隐睾症患儿的临床、生物学和遗传学分析。
PLoS One. 2011;6(8):e23292. doi: 10.1371/journal.pone.0023292. Epub 2011 Aug 10.
2
Cryptorchidism: pathogenesis, diagnosis, treatment and prognosis.隐睾症:发病机制、诊断、治疗和预后。
Urol Clin North Am. 2010 May;37(2):183-93. doi: 10.1016/j.ucl.2010.03.002.
3
Mutational analysis of steroidogenic factor 1 (NR5a1) in 24 boys with bilateral anorchia: a French collaborative study.24例双侧无睾症男孩类固醇生成因子1(NR5a1)的突变分析:一项法国合作研究。
Hum Reprod. 2007 Dec;22(12):3255-61. doi: 10.1093/humrep/dem278. Epub 2007 Oct 16.
4
Bilateral anorchia in infancy: occurence of micropenis and the effect of testosterone treatment.婴儿期双侧无睾症:小阴茎的发生及睾酮治疗的效果
J Pediatr. 2006 Nov;149(5):687-91. doi: 10.1016/j.jpeds.2006.07.044.
5
Testicular regression syndrome--a pathological study of 77 cases.睾丸退化综合征——77例病例的病理学研究
Histopathology. 1991 Sep;19(3):269-72. doi: 10.1111/j.1365-2559.1991.tb00033.x.

无籽兰花:无睾成年男性的问题

Seedless orchids: Issues in the anorchid adult.

作者信息

Altamash Shaikh, Kumar K V S Hari

机构信息

Saifee Hospital, Mumbai, Maharashtra, India.

Department of Endocrinology, Command Hospital, Lucknow, Uttar Pradesh, India.

出版信息

Indian J Endocrinol Metab. 2013 Dec;17(Suppl 3):S685-7. doi: 10.4103/2230-8210.123568.

DOI:10.4103/2230-8210.123568
PMID:24910839
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4046610/
Abstract

Disorders of sexual differentiation (DSD) are among the challenging problems in the field of endocrinology. When presenting late in an adult the therapeutic as well as diagnostic issues may be different and difficult. Bilateral anorchia is rare. The desire of future parenting is a real challenge when such patients ask for their own biological generations. This case depicts the late presentation of DSD in an anorchid adult and the management issues.

摘要

性分化障碍(DSD)是内分泌学领域中具有挑战性的问题之一。当在成人期出现较晚时,治疗和诊断问题可能会有所不同且较为困难。双侧无睾症很罕见。当这类患者希望拥有自己的亲生后代时,未来生育的愿望是一个真正的挑战。本病例描述了一名无睾症成年患者DSD的晚期表现及管理问题。