Pierre Ketsia, Borer Joseph, Phelps Andrew, Chow Jeanne S
Department of Radiology, Boston Children's Hospital, 300 Longwood Ave., Boston, MA, 02115, USA,
Pediatr Radiol. 2014 Jul;44(7):768-86; quiz 765-7. doi: 10.1007/s00247-014-2892-5. Epub 2014 Jun 18.
Bladder exstrophy is a rare malformation characterized by an infra-umbilical abdominal wall defect, incomplete closure of the bladder with mucosa continuous with the abdominal wall, epispadias, and alterations in the pelvic bones and muscles. It is part of the exstrophy-epispadias complex, with cloacal exstrophy on the severe and epispadias on the mild ends of the spectrum. Bladder exstrophy is the most common of these entities and is more common in boys. The goal of this paper is to describe common methods of repair and to provide an imaging review of the postoperative appearances.
膀胱外翻是一种罕见的畸形,其特征为脐下腹壁缺损、膀胱未完全闭合且黏膜与腹壁相连、尿道上裂以及骨盆骨骼和肌肉的改变。它是膀胱外翻-尿道上裂复合体的一部分,泄殖腔外翻处于该谱系的严重端,尿道上裂处于轻度端。膀胱外翻是这些病症中最常见的,且在男性中更为常见。本文的目的是描述常见的修复方法并提供术后表现的影像学综述。