Senveli E, Altinörs N, Kars Z, Arda N, Türker A, Cinar N, Yalniz Z
Clinic of Neurosurgery, Social Security Hospital, Ankara, Turkey.
Neurosurgery. 1989 Jan;24(1):99-101. doi: 10.1227/00006123-198901000-00017.
We present 6 patients with a definite diagnosis of von Recklinghausen's neurofibromatosis. All of them had aqueductal stenosis and hydrocephalus requiring surgical intervention because of clinical signs of increased intracranial pressure confirmed by pressure measurements.
我们报告6例确诊为冯·雷克林霍增氏神经纤维瘤病的患者。他们均患有导水管狭窄和脑积水,由于压力测量证实存在颅内压升高的临床体征,均需要进行手术干预。