Shelton C, Luxford W M, Tonokawa L L, Lo W W, House W F
Otologic Medical Group, Inc., Los Angeles, CA 90057.
Otolaryngol Head Neck Surg. 1989 Mar;100(3):227-31. doi: 10.1177/019459988910000310.
We suggest a new explanation for the lack of auditory response to electric stimulation in children with cochlear implants: the very narrow internal auditory canal, 1 to 2 mm in diameter, and the probable absence of the cochlear nerve. This defect can be seen on high-resolution computed tomographic x-ray studies and may represent aplasia of the auditory-vestibular nerve. We report on eight children with this anomaly, three of whom have received implants and failed to respond with a sensation of sound. Identification of this problem on screening x-ray films is a contraindication to cochlear implantation for auditory stimulation.