Molnar Adrian, Encică Svetlana, Kovács Emese, Manole Simona, Săcui Diana, Mureşan Ioan, Scridon Traian
Clinic of Cardiovascular Surgery, "Niculae Stancioiu" Heart Institute, Cluj-Napoca, Romania;
Rom J Morphol Embryol. 2014;55(2):463-7.
Papillary fibroelastoma is a rare, benign cardiac tumor typically found on the heart valves, which is usually discovered incidentally on echocardiography. The clinical presentation of cardiac papillary fibroelastoma varies from no symptoms to severe embolic sequelae. We report the case of a 55-year-old female patient, with a suspicion of pulmonary embolism one year before, presently admitted to the hospital for mild respiratory symptoms; the trans-esophageal echocardiography (TEE) revealed a 10/10 mm tumoral mass attached on the pulmonary valve, confirmed also by the contrast-enhanced magnetic resonance imaging (MRI). Considering the embolization risk, we decided surgical removal, with favorable outcome. The pathologic exam of the removed tumor established the diagnosis of papillary fibroelastoma. The clinical and imaging assessment one month after surgery were within normal limits. The surgical removal of the papillary fibroelastoma of the pulmonary valve is mandatory for the elimination of embolization risk. The intervention is relatively secure, with low rates of morbidity and mortality.
乳头状纤维弹性瘤是一种罕见的良性心脏肿瘤,通常发现于心脏瓣膜,常于超声心动图检查时偶然发现。心脏乳头状纤维弹性瘤的临床表现从无症状到严重的栓塞后遗症不等。我们报告一例55岁女性患者,一年前怀疑有肺栓塞,目前因轻度呼吸道症状入院;经食管超声心动图(TEE)显示一个10/10毫米的肿瘤附着在肺动脉瓣上,对比增强磁共振成像(MRI)也证实了这一点。考虑到栓塞风险,我们决定进行手术切除,结果良好。切除肿瘤的病理检查确诊为乳头状纤维弹性瘤。术后一个月的临床和影像学评估均在正常范围内。为消除栓塞风险,肺动脉瓣乳头状纤维弹性瘤的手术切除是必要的。该干预相对安全,发病率和死亡率较低。