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脂质肺炎作为洛伦佐油疗法在一名肾上腺脑白质营养不良患者中的并发症。

Lipoid pneumonia as a complication of Lorenzo's oil therapy in a patient with adrenoleukodystrophy.

作者信息

Majori Maria, Scarascia Alessandro, Anghinolfi Miriam, Pisi Roberta, Gnetti Letizia, Casalini Angelo Gianni

机构信息

*Pulmonology and Thoracic Endoscopy Unit †Respiratory Disease Unit ‡Pathologic Anatomy Unit, University Hospital of Parma, Parma, Italy.

出版信息

J Bronchology Interv Pulmonol. 2014 Jul;21(3):271-3. doi: 10.1097/LBR.0000000000000084.

DOI:10.1097/LBR.0000000000000084
PMID:24992138
Abstract

Lipoid pneumonia (LP) is a rare exogenous condition caused by inhalation or aspiration of lipid material into the lungs. It is often associated with the therapeutic use of different types of oil, and the diagnosis is based on the demonstration of lipid-laden macrophages in bronchoalveolar lavage fluid. We reported the case of a 39-year-old male with X-linked adrenoleukodystrophy who developed LP secondary to the use of Lorenzo's oil. To our knowledge, the association between the use of Lorenzo's oil and LP has never been reported in literature.

摘要

类脂性肺炎(LP)是一种罕见的外源性疾病,由脂质物质吸入或误吸进入肺部所致。它常与不同类型油类的治疗应用相关,诊断基于支气管肺泡灌洗 fluid 中发现含脂巨噬细胞。我们报告了一例39岁患有X连锁肾上腺脑白质营养不良的男性患者,其因使用洛伦佐油而继发LP。据我们所知,使用洛伦佐油与LP之间的关联在文献中从未有过报道。 (注:原文中“bronchoalveolar lavage fluid”翻译为“支气管肺泡灌洗 fluid”,此处“fluid”可能是“fluid”拼写错误,正确应为“fluid”即“液体”,完整应是“支气管肺泡灌洗液” )

相似文献

1
Lipoid pneumonia as a complication of Lorenzo's oil therapy in a patient with adrenoleukodystrophy.脂质肺炎作为洛伦佐油疗法在一名肾上腺脑白质营养不良患者中的并发症。
J Bronchology Interv Pulmonol. 2014 Jul;21(3):271-3. doi: 10.1097/LBR.0000000000000084.
2
Lorenzo's oil and lymphocytopenia.洛伦佐的油与淋巴细胞减少症
N Engl J Med. 1994 Feb 24;330(8):577. doi: 10.1056/NEJM199402243300819.
3
Follow-up of 89 asymptomatic patients with adrenoleukodystrophy treated with Lorenzo's oil.对89例接受洛伦佐油治疗的无症状肾上腺脑白质营养不良患者的随访。
Arch Neurol. 2005 Jul;62(7):1073-80. doi: 10.1001/archneur.62.7.1073.
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Thrombocytopenia associated with use of Lorenzo's oil.与使用洛伦佐油相关的血小板减少症。
Am J Hematol. 1993 Dec;44(4):290-1. doi: 10.1002/ajh.2830440417.
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Very long chain fatty acids in X-linked adrenoleukodystrophy brain after treatment with Lorenzo's oil.使用洛伦佐油治疗后X连锁肾上腺脑白质营养不良症患者大脑中的极长链脂肪酸
Ann Neurol. 1994 Nov;36(5):741-6. doi: 10.1002/ana.410360509.
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Severely depressed natural killer cell activity of patients with adrenoleukodystrophy under treatment with Lorenzo's oil.接受洛伦佐油治疗的肾上腺脑白质营养不良患者自然杀伤细胞活性严重降低。
J Inherit Metab Dis. 1995;18(1):101-2. doi: 10.1007/BF00711394.
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Bleeding in a patient taking Lorenzo's oil: evidence for a vascular defect.服用洛伦佐之油的患者出血:血管缺陷的证据。
Postgrad Med J. 1996 Feb;72(844):113-4. doi: 10.1136/pgmj.72.844.113.
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Lorenzo's oil: advances in the treatment of neurometabolic disorders.洛伦佐之油:神经代谢紊乱治疗的进展
Arch Neurol. 2005 Jul;62(7):1045-6. doi: 10.1001/archneur.62.7.1045.
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[Adrenoleukodystrophy: Lorenzo's Oil].[肾上腺脑白质营养不良:洛伦佐的油]
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Treatment of X-linked adrenoleukodystrophy with Lorenzo's oil.用洛伦佐油治疗X连锁肾上腺脑白质营养不良。
J Neurol Neurosurg Psychiatry. 1999 Sep;67(3):279-80. doi: 10.1136/jnnp.67.3.279.

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Adult exogenous lipoid pneumonia: A rare and underrecognized entity in cytology - A case series.成人外源性类脂性肺炎:细胞学中一种罕见且未被充分认识的疾病——病例系列报道
Cytojournal. 2018 Jul 13;15:17. doi: 10.4103/cytojournal.cytojournal_29_17. eCollection 2018.
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Plugs of the Air Passages: A Clinicopathologic Review.气道栓子:临床病理综述
Chest. 2016 Nov;150(5):1141-1157. doi: 10.1016/j.chest.2016.07.003. Epub 2016 Jul 19.