Department of Cardiology, Shanghai Children's Hospital, Shanghai Jiao Tong University, West Beijing Road 1400-24, Shanghai 200040, PR China.
Department of Cardiology, Shanghai Children's Hospital, Shanghai Jiao Tong University, West Beijing Road 1400-24, Shanghai 200040, PR China.
Heart Lung. 2014 Jul-Aug;43(4):367-70. doi: 10.1016/j.hrtlng.2014.04.018.
Primary pulmonary vein stenosis (PVS) presenting in childhood is uncommon and is related to premature with bronchopulmonary dysplasia (BPD). Here we present a premature infant with primary PVS and without BPD. In our case, a 19-month-old girl was diagnosed with PVS, atrial septal defect and patent arterial duct by echocardiography and selective pulmonary artery angiography. Interestingly in the first 2 month after birth, there was no clue of PVS by bed echocardiography in the patient. It is important to focus on the pulmonary vein blood velocity in premature infants and very low birth weight infants even without BPD.
儿童原发性肺静脉狭窄（PVS）并不常见，与支气管肺发育不良（BPD）有关。本文报道了一例无 BPD 的原发性 PVS 早产儿。本病例为 19 月龄女性，超声心动图和选择性肺动脉造影诊断为 PVS、房间隔缺损和动脉导管未闭。有趣的是，患儿出生后前 2 个月床旁超声心动图均未见 PVS 征象。即使没有 BPD，对早产儿和极低出生体重儿也应重视肺静脉血流速度。
