Kempter F, Möhring K, Müller-Wiefel D E
Urologische Klinik des Chirurgischen Zentrums, Universität, Heidelberg.
Monatsschr Kinderheilkd. 1989 May;137(5):289-92.
Urinary tract involvement in neurofibromatosis is rare. We found 51 cases documented in the literature, the majority of these (n = 31) were children. More than half of these (n = 18) developed upper urinary tract obstruction. A report is given of a 10-month-old boy with neurofibromatosis of the bladder. Treatment consisted in radical surgery with cystoprostatectomy and uretero-transureterocutaneostomy. Follow-up of 10 years presents a good result. The different modalities of treatment are reviewed in the literature.
神经纤维瘤病累及泌尿系统较为罕见。我们在文献中发现了51例相关病例，其中大多数（n = 31）为儿童。这些病例中超过一半（n = 18）出现上尿路梗阻。本文报告了一名患有膀胱神经纤维瘤病的10个月大男孩。治疗方法为行根治性手术，包括膀胱前列腺切除术及输尿管-输尿管皮肤造口术。10年的随访结果良好。本文对文献中不同的治疗方式进行了综述。
