Mahore Amit, Ramdasi Raghvendra Vijayrao, Pauranik Anvita, Epari Shridhar
Seth G.S. Medical College & KEM Hospital, Mumbai, Maharashtra, India.
Department of Neurosurgery, Seth G.S. Medical College & KEM Hospital, Mumbai, Maharashtra, India.
BMJ Case Rep. 2014 Jul 9;2014:bcr2014205175. doi: 10.1136/bcr-2014-205175.
We report a unique case of primary extradural angiosarcoma of posterior fossa manifesting as extradural haematoma in a 12-year-old boy who presented with acute onset headache, vomiting, nuchal rigidity and altered sensorium. The patient underwent a retromastoid suboccipital craniotomy on emergency basis, and the lesion was excised completely. Histopathology and immunohistochemistry revealed an angiosarcoma, following which radiation therapy was given. The patient showed complete clinical and neurological improvement. At a follow-up of 2 years he is in good health without any sign of regrowth.