Mahore Amit, Ramdasi Raghvendra Vijayrao, Pauranik Anvita, Epari Shridhar
Seth G.S. Medical College & KEM Hospital, Mumbai, Maharashtra, India.
Department of Neurosurgery, Seth G.S. Medical College & KEM Hospital, Mumbai, Maharashtra, India.
BMJ Case Rep. 2014 Jul 9;2014:bcr2014205175. doi: 10.1136/bcr-2014-205175.
We report a unique case of primary extradural angiosarcoma of posterior fossa manifesting as extradural haematoma in a 12-year-old boy who presented with acute onset headache, vomiting, nuchal rigidity and altered sensorium. The patient underwent a retromastoid suboccipital craniotomy on emergency basis, and the lesion was excised completely. Histopathology and immunohistochemistry revealed an angiosarcoma, following which radiation therapy was given. The patient showed complete clinical and neurological improvement. At a follow-up of 2 years he is in good health without any sign of regrowth.
我们报告了一例罕见的后颅窝原发性硬膜外血管肉瘤病例,该病例表现为硬膜外血肿,患者为一名12岁男孩,出现急性头痛、呕吐、颈部强直和意识改变。患者在紧急情况下接受了乳突后枕下开颅手术,病变被完全切除。组织病理学和免疫组织化学检查显示为血管肉瘤,随后进行了放射治疗。患者临床和神经功能完全改善。在2年的随访中,他身体健康,没有任何复发迹象。