Lee Chan-Hee, Son Jang-Won, Park Jong-Seon
Department of Cardiology, Yeungnam University Hospital, 170, Hyeonchungro, Nam-gu, Daegu 705-717, Korea.
BMC Cardiovasc Disord. 2014 Aug 20;14:104. doi: 10.1186/1471-2261-14-104.
Right-sided aortic arch is a rare congenital defect usually diagnosed incidentally in adults; it is often asymptomatic unless aneurismal disease develops. In half the cases, an aberrant left subclavian artery arises from a Kommerell's diverticulum; in these cases, congenital heart anomaly is very rarely present.
We report a case of incidentally-detected right-sided aortic arch with multiple vascular anomalies including left subclavian artery originating from a Kommerell's diverticulum, supra-sinus origin of coronary arteries and coronary arteriovenous fistula.
Through comprehensive 3-dimensional reconstruction of the aortic arch and surrounding structures we defined anatomical relationships, which is useful for follow-up and treatment.
右位主动脉弓是一种罕见的先天性缺陷，通常在成人中偶然被诊断出来；除非发生动脉瘤疾病，否则通常无症状。在半数病例中，异常的左锁骨下动脉起源于Kommerell憩室；在这些病例中，先天性心脏异常非常罕见。
我们报告一例偶然发现的右位主动脉弓合并多种血管异常的病例，包括起源于Kommerell憩室的左锁骨下动脉、冠状动脉窦上起源以及冠状动脉动静脉瘘。
通过对主动脉弓及其周围结构进行全面的三维重建，我们明确了解剖关系，这对随访和治疗很有帮助。
