Meiselbach Heike, Vogel Nico, Langlhofer Georg, Stangl Sabine, Schleyer Barbara, Bahnassawy Lamia'a, Sticht Heinrich, Breitinger Hans-Georg, Becker Cord-Michael, Villmann Carmen
From Bioinformatics and.
Institute of Biochemistry, Emil Fischer Center, Friedrich-Alexander University Erlangen-Nürnberg, Fahrstrasse 17, 91054 Erlangen, Germany.
J Biol Chem. 2014 Oct 17;289(42):29135-47. doi: 10.1074/jbc.M114.559138. Epub 2014 Aug 20.
Cys loop receptors are pentameric arrangements of independent subunits that assemble into functional ion channels. Each subunit shows a domain architecture. Functional ion channels can be reconstituted even from independent, nonfunctional subunit domains, as shown previously for GlyRα1 receptors. Here, we demonstrate that this reconstitution is not restricted to α1 but can be transferred to other members of the Cys loop receptor family. A nonfunctional GlyR subunit, truncated at the intracellular TM3-4 loop by a premature stop codon, can be complemented by co-expression of the missing tail portion of the receptor. Compared with α1 subunits, rescue by domain complementation was less efficient when GlyRα3 or the GABAA/C subunit ρ1 was used. If truncation disrupted an alternative splicing cassette within the intracellular TM3-4 loop of α3 subunits, which also regulates receptor desensitization, functional rescue was not possible. When α3 receptors were restored by complementation using domains with and without the spliced insert, no difference in desensitization was found. In contrast, desensitization properties could even be transferred between α1/α3 receptor chimeras harboring or lacking the α3 splice cassette proving that functional rescue depends on the integrity of the alternative splicing cassette in α3. Thus, an intact α3 splicing cassette in the TM3-4 loop environment is indispensable for functional rescue, and the quality of receptor restoration can be assessed from desensitization properties.
半胱氨酸环受体是由独立亚基组成的五聚体结构,这些亚基组装成功能性离子通道。每个亚基都呈现出一种结构域架构。即使是从独立的、无功能的亚基结构域也能重构出功能性离子通道,如先前针对甘氨酸受体α1所展示的那样。在此,我们证明这种重构并不局限于α1,而是可以扩展到半胱氨酸环受体家族的其他成员。一个无功能的甘氨酸受体亚基,由于提前终止密码子在细胞内TM3 - 4环处被截断,通过共表达受体缺失的尾部部分可以得到互补。与α1亚基相比,当使用甘氨酸受体α3或GABAA/C亚基ρ1时,通过结构域互补进行的拯救效率较低。如果截断破坏了α3亚基细胞内TM3 - 4环内的一个可变剪接盒,而该剪接盒也调节受体脱敏,那么功能性拯救是不可能的。当使用带有和不带有剪接插入片段的结构域通过互补来恢复α3受体时,未发现脱敏方面的差异。相反,脱敏特性甚至可以在含有或不含有α3剪接盒的α1/α3受体嵌合体之间转移,这证明功能性拯救取决于α3中可变剪接盒的完整性。因此,TM3 - 4环环境中完整的α3剪接盒对于功能性拯救是不可或缺的,并且可以从脱敏特性评估受体恢复的质量。