Papagrigorakis M J, Daliouris C P, Spyropoulos N D
Odontostomatol Proodos. 1989 Oct;43(5):451-8.
Manifestations from the craniofacial complex in patients presenting with the Rubinstein-Taybi syndrome, are of a special interest to the dentist as they involve structures of the oral cavity. On the occasion of three cases that exhibit some of the characteristic signs of this syndrome, the authors provide an extensive review of the related literature. Also, the specific morphology of the face, fingers, and oral structures of these patients is described, as well as, the findings from their cephalometric radiographs. These findings are indicative of a retrognathic face with severe dental crowding requiring extensive orthodontic treatment.
患有鲁宾斯坦-泰比综合征的患者,其颅面复合体的表现对牙医来说具有特殊意义,因为这些表现涉及口腔结构。在三例展现出该综合征某些特征性体征的病例中,作者对相关文献进行了全面综述。此外,还描述了这些患者面部、手指和口腔结构的具体形态,以及他们头颅侧位片的检查结果。这些结果表明患者面部后缩且牙齿严重拥挤,需要进行广泛的正畸治疗。