Fernández-Menéndez Santiago, Redondo-Robles Laura, García-Santiago Rocío, García-González María Ángeles, Arés-Luque Adrián
Department of Neurology, University Hospital of León, León, Spain.
Department of Neurology, University Hospital of León, León, Spain.
Am J Otolaryngol. 2014 Nov-Dec;35(6):810-3. doi: 10.1016/j.amjoto.2014.08.002. Epub 2014 Aug 20.
Isolated cranial nerve involvement in multiple sclerosis (MS) patients is not frequent. Deafness is considered to be uncommon in MS patients. We have reviewed the sensorineural hearing loss episodes that had been thoroughly investigated in our hospital in the last 5 years. We present three cases of sensorineural hearing loss in patients with MS and compare them with other previously reported and discuss this uncommon symptom. The cases that we present were firstly evaluated by an otolaryngologist. A lesion is seen at the root-entry zone of the eighth cranial nerve in only one case, but no lesions are seen in the other cases. A retrocochlear demyelinating disorder was demonstrated in the two patients in whom brainstem auditory evoked potentials were performed. All patients recovered at least partially their hearing functions.
孤立性颅神经受累在多发性硬化症(MS)患者中并不常见。耳聋在MS患者中被认为不常见。我们回顾了过去5年在我院经过全面调查的感音神经性听力损失病例。我们报告3例MS患者的感音神经性听力损失病例,并将其与之前报道的病例进行比较,探讨这种不常见的症状。我们所报告的病例首先由耳鼻喉科医生进行评估。仅1例在第八颅神经的神经根进入区可见病变,其他病例未见病变。在2例行脑干听觉诱发电位检查的患者中证实存在蜗后脱髓鞘疾病。所有患者的听力功能至少部分恢复。