Department of Anesthesiology and Reanimation, Kocaeli University Faculty of Medicine, Kocaeli, Turkey.
Balkan Med J. 2013 Sep;30(3):321-2. doi: 10.5152/balkanmedj.2013.6960. Epub 2013 Sep 1.
Pseudo-TORCH syndrome is a rare, chronic disorder that is characterised by dimorphic features such as microcephaly, intracranial calcification, seizures, mental retardation, hepatosplenomegaly and coagulation disorders.
We present the anaesthetic management of a forty day-old boy with Pseudo-TORCH syndrome during magnetic resonance imaging. Microcephaly, growth failure, high palate and bilateral rales in the lungs were detected in pre-anaesthetic physical examination. The peripheral oxygen saturation was 88-89% in room-air and was 95% in a hood with 5 L/min oxygen. We planned general anaesthesia to ensure immobility during magnetic resonance imaging. After standard monitoring, general anaesthesia was induced with 8% sevoflurane in 100% O2. After an adequate depth of anaesthesia was reached, we inserted a supraglottic airway device to avoid intubation without the use of a muscle relaxant.
In patients with Pseudo-TORCH syndrome, the perioperative anaesthetic risk was increased. We believe that using a supraglottic airway device to secure the airway is less invasive than intubation, and can be performed without the need of muscle relaxants.
伪 TORCH 综合征是一种罕见的慢性疾病，其特征为多种形态学特征，如小头畸形、颅内钙化、癫痫发作、智力迟钝、肝脾肿大和凝血障碍。
我们介绍了一例四十天大的患有伪 TORCH 综合征的男孩在磁共振成像检查期间的麻醉管理。在麻醉前体格检查中发现存在小头畸形、生长发育不良、高腭和双肺啰音。在空气环境中，外周血氧饱和度为 88-89%，在 5 L/min 氧气的头罩下为 95%。我们计划全身麻醉以确保磁共振成像检查期间的无移动性。在进行标准监测后，使用 100%氧气中的 8%七氟醚诱导全身麻醉。在达到足够的麻醉深度后，我们插入了一种声门上气道装置以避免在不使用肌肉松弛剂的情况下进行插管。
在患有伪 TORCH 综合征的患者中，围手术期麻醉风险增加。我们认为使用声门上气道装置来确保气道比插管更具侵入性，并且可以在不需要肌肉松弛剂的情况下进行。
