Lee Chee-Hoon, Seo Dong Ju, Bang Ji Hyun, Goo Hyun Woo, Park Jeong-Jun
Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine.
Department of Radiology, Asan Medical Center, University of Ulsan College of Medicine.
Korean J Thorac Cardiovasc Surg. 2014 Aug;47(4):389-93. doi: 10.5090/kjtcs.2014.47.4.389. Epub 2014 Aug 5.
Retroesophageal aortic arch, in which the aortic arch crosses the midline behind the esophagus to the contralateral side, is a rare form of vascular anomaly. The complete form may cause symptoms by compressing the esophagus or the trachea and need a surgical intervention. We report a rare case of a hypoplastic left heart syndrome variant with the left retroesophageal circumflex aortic arch in which the left aortic arch, retroesophageal circumflex aorta, and the right descending aorta with the aberrant right subclavian artery encircle the esophagus completely, thus causing central bronchial compression. Bilateral pulmonary artery banding and subsequent modified Norwood procedure with extensive mobilization and creation of the neo-aorta were performed. As a result of the successful translocation of the aorta, the airway compression was relieved. The patient underwent the second-stage operation and is doing well currently.
食管后主动脉弓是一种罕见的血管异常形式,其中主动脉弓在食管后方越过中线至对侧。完整形式可能通过压迫食管或气管而引起症状,需要手术干预。我们报告一例罕见的左心发育不全综合征变异型病例,其左主动脉弓呈食管后回旋状,左主动脉弓、食管后回旋主动脉以及伴有迷走右锁骨下动脉的右降主动脉完全环绕食管,从而导致中央支气管受压。进行了双侧肺动脉环扎术,随后进行了改良诺伍德手术,广泛游离并构建了新主动脉。由于主动脉成功移位,气道压迫得以缓解。患者接受了二期手术,目前情况良好。