Chirino-Romo Jorge, Bertrand-Noriega Federico, Benita-Bordes Antonio, Orozco-Olguín Pamela, Paz-Martínez Mauricio
Cirugía General, Hospital Ángeles del Pedregal, México, DF, Mexico.
Cirugía Cardiotorácica, Hospital Central Militar, México, DF, Mexico.
Cir Cir. 2014 Sep-Oct;82(5):537-40.
Thoracic lymphangioma is a rare benign disease representing only 0.7-4.5% of all mediastinal tumors. Its etiology is currently unknown. Most are asymptomatic at first, and the condition is common in the pediatric age. We present a case to document this rare disease and describe the literature.
We present the case of a 5-year-old female without clinically significant medical history. The patient attended a routine physician visit where a heart murmur was discovered. A diagnostic protocol was initiated, finding a mass on chest x-rays, apparently with an intrathoracic localization. Chest computed tomography confirms a tumor of 13 × 11 cm localized in the anterior mediastinum. Laboratory studies were within normal parameters. Complete surgical resection was decided upon and histopathological diagnosis of cavernosum lymphangioma is confirmed. The patient experienced an adequate evolution without evidence of relapse at this timeConclusion: Characteristics of the case shown are consistent with those reported in the literature. Diagnostic management as well as the surgical plan was successful without presenting morbidity so far.
胸段淋巴管瘤是一种罕见的良性疾病，仅占所有纵隔肿瘤的0.7%-4.5%。其病因目前尚不清楚。大多数患者起初无症状，且该疾病在儿童期较为常见。我们报告一例病例以记录这种罕见疾病并阐述相关文献。
我们报告一例5岁女性患者，其无具有临床意义的病史。该患者在常规就诊时被发现有心脏杂音。启动了诊断流程，胸部X光检查发现一个肿块，显然位于胸腔内。胸部计算机断层扫描证实一个13×11厘米的肿瘤位于前纵隔。实验室检查结果在正常范围内。决定进行完整的手术切除，术后病理诊断为海绵状淋巴管瘤。患者恢复良好，目前无复发迹象。结论：该病例的特征与文献报道一致。诊断管理及手术方案成功，目前未出现并发症。
