Arreo Del Val V, Avila-Alvarez A, Schteffer L R, Santos F, Deiros L, Del Cerro M J
Department of Pediatric Cardiology, La Paz Children's Hospital, Madrid, Spain.
Neonatal Intensive Care Unit, Department of Neonatology, La Paz Children's Hospital, Madrid, Spain.
J Perinatol. 2014 Oct;34(10):795-7. doi: 10.1038/jp.2014.94.
Alveolar capillary dysplasia with misalignment of the pulmonary veins (ACD/MPV) is a rare and lethal cause of refractory pulmonary hypertension of the newborn. We describe the clinical course of a neonate with refractory pulmonary hypertension diagnosed with ACD/MPV, aortic coarctation and other not previously reported associated malformations.
肺泡毛细血管发育不良伴肺静脉错位(ACD/MPV)是新生儿难治性肺动脉高压的一种罕见且致命的病因。我们描述了一名诊断为ACD/MPV、主动脉缩窄及其他先前未报道的相关畸形的难治性肺动脉高压新生儿的临床病程。