Akasaka T, Mitsuishi T, Nakajima H, Suzuki R, Shimizu S
Second Department of Surgery, Teikyo University School of Medicine, Tokyo, Japan.
J Cardiovasc Surg (Torino). 1989 Nov-Dec;30(6):945-7.
An unusual case of a 38-year-old woman with Turner's syndrome associated with aneurysmal dilation of the left subclavian artery is presented. Aortography revealed a fusiform aneurysm in the proximal segment of the left subclavian artery, which was as long as 6 cm. The diagnosis of Turner's syndrome was postoperatively confirmed by chromosomal study, which showed 45X0. The aneurysm was successfully removed and reconstruction was done by interposition of a woven Dacron graft, 8 mm in diameter and 6 cm in length, between the thoracic aorta and subclavian artery just proximal to the thoracic outlet. Microscopic findings of the resected tissue of the subclavian artery revealed deposition of acid mucopolysaccharide in the intima and media.
本文报告了一例38岁特纳综合征女性患者，其伴有左锁骨下动脉动脉瘤样扩张。主动脉造影显示左锁骨下动脉近端有一梭形动脉瘤，长6厘米。术后经染色体检查确诊为特纳综合征，结果显示为45X0。成功切除动脉瘤，并通过在胸主动脉和锁骨下动脉胸段出口近端之间置入一段直径8毫米、长6厘米的编织涤纶移植物进行重建。锁骨下动脉切除组织的显微镜检查发现内膜和中膜有酸性粘多糖沉积。
