Petraitienė Indrė, Barauskas Giedrius, Gulbinas Antanas, Malcius Dalius, Hussain Khalid, Verkauskas Gilvydas, Verkauskienė Rasa
Institute of Endocrinology, Medical Academy, Lithuanian University of Health Sciences, Kaunas, Lithuania.
Department of Surgery, Medical Academy, Lithuanian University of Health Sciences, Kaunas, Lithuania.
Medicina (Kaunas). 2014;50(3):190-5. doi: 10.1016/j.medici.2014.08.006. Epub 2014 Aug 13.
Hyperinsulinism is the most common cause of hypoglycemia in infants. In many cases conservative treatment is not effective and surgical intervention is required. Differentiation between diffuse and focal forms and localization of focal lesions are the most important issues in preoperative management. We present a case of persistent infancy hyperinsulinism. Clinical presentation, conservative treatment modalities, diagnostic possibilities of focal and diffuse forms, and surgical treatment, which led to total recovery, are discussed.
高胰岛素血症是婴儿低血糖最常见的原因。在许多情况下,保守治疗无效,需要手术干预。区分弥漫性和局灶性形式以及局灶性病变的定位是术前管理中最重要的问题。我们报告一例持续性婴儿高胰岛素血症病例。讨论了临床表现、保守治疗方式、局灶性和弥漫性形式的诊断可能性以及导致完全康复的手术治疗。