Münter Kristine, Johansen Jakob, Atke Anders, Fuhrmann Lone
Anæstesiologisk Afdeling I, Herlev Hospital, Herlev Ringvej 75, 2730 Herlev. E-mail:
Ugeskr Laeger. 2014 Oct 6;176(41).
We describe a case of a first time parturient with Klippel-Feil syndrome (KFS). KFS is defined by fusion of cervical vertebrae and the clinical triad of low posterior hairline, short wide neck and limited neck movement. KFS represents a complex challenging anaesthesiologic condition due to limited movement of the neck and the risk of irreversible neurologic sequelae if manipulated, as well as unpredictable effect of neuroaxial anaesthesia. We recommend awake fiberoptic intubation for airway management in this rare disorder and stress the necessity of early anaesthesiologic assessment in any cervical spine disorder that might need airway management.
我们描述了一例首次分娩的患有Klippel-Feil综合征(KFS)的产妇。KFS的定义是颈椎融合以及低后发际线、短而宽的颈部和颈部活动受限这一临床三联征。由于颈部活动受限,若操作不当有发生不可逆神经后遗症的风险,以及神经轴索麻醉效果不可预测,KFS是一种复杂且具有挑战性的麻醉情况。我们建议在这种罕见疾病中采用清醒纤维支气管镜插管进行气道管理,并强调对于任何可能需要气道管理的颈椎疾病,早期进行麻醉评估的必要性。