Nirupam Nilay, Pemde Harish, Chandra Jagdish
Division of Pediatric Hematology, Department of Pediatrics, Lady Hardinge Medical College and Associated Kalawati Saran Children's Hospital, New Delhi, 110001 India.
Indian J Hematol Blood Transfus. 2014 Sep;30(Suppl 1):54-6. doi: 10.1007/s12288-013-0245-4. Epub 2013 Mar 7.
Spontaneous spinal epidural hematoma (SSEH) is a rare complication in patients of haemophilia. We report the case of a 9-year-old boy with severe haemophilia B who presented with acute abdomen of 5 days duration. Acute onset of neck/back pain,walking impairment and urinary retention has usually been described as symptom complex in SSEH. The hematoma was identified by magnetic resonance imaging of the spinal column. Our case calls attention to recognition of abdominal pain (with no other localizing features) as initial symptom of SSEH and prompt evaluation and management before more overt symptoms of spinal cord compression becomes evident.
自发性脊髓硬膜外血肿(SSEH)是血友病患者中一种罕见的并发症。我们报告了一例9岁重度B型血友病男孩的病例,该男孩出现了持续5天的急腹症。颈部/背部疼痛急性发作、行走障碍和尿潴留通常被描述为SSEH的症状复合体。通过脊柱磁共振成像确定了血肿。我们的病例提醒人们注意,将腹痛(无其他定位特征)识别为SSEH的初始症状,并在脊髓压迫的更明显症状出现之前进行及时评估和处理。