Dousek Robert, Tuma Jiri, Planka Ladislav, Husek Karel, Sterba Jaroslav, Penka Igor
Departments of *Pediatric Surgery †Pathology ‡Pediatric Oncology §Surgery, The University Hospital Brno, Brno, Czech Republic.
J Pediatr Hematol Oncol. 2015 Mar;37(2):e121-4. doi: 10.1097/MPH.0000000000000275.
Inflammatory myofibroblastic tumor (IMT) is a rare mesenchymal disease of low malignancy consisting of inflammatory cells inside a mesenchymal stroma comprising myofibroblasts. Biological behavior is variable, recurrence is uncommon, metastatic disease is rare. Treatment strategy is based on the status of low-grade malignant tumor. Radical surgery is considered to be the principal treatment modality, except if it requires a mutilating procedure. Only 6 cases of pediatric patients treated for IMT of the esophagus have been reported in English-language literature. Herein, a case of a 13-year-old boy with an IMT of the esophagus is presented.
炎性肌纤维母细胞瘤（IMT）是一种罕见的低恶性间叶性疾病，由包含肌成纤维细胞的间叶基质内的炎性细胞组成。生物学行为多变，复发不常见，转移性疾病罕见。治疗策略基于低级别恶性肿瘤的状况。除了需要进行致残性手术外，根治性手术被认为是主要的治疗方式。英文文献中仅报道了6例接受食管IMT治疗的儿科患者。本文介绍了1例13岁患有食管IMT的男孩病例。
