Tycko B, Reynolds T C, Smith S D, Sklar J
Department of Pathology, Stanford University, California 94305.
J Exp Med. 1989 Feb 1;169(2):369-77. doi: 10.1084/jem.169.2.369.
Chromosomal translocations in lymphoid tumors frequently result from recombination between a normally rearranging antigen receptor gene and a normally non-rearranging second locus. The possibility that the lymphocyte recombinase apparatus plays a role in determining the position of breakage at the second locus has been a matter of controversy because of the inconsistent presence of heptamer-like recognition sequences adjoining breakpoints at this site. To further investigate this issue, sites of DNA recombination were analyzed in both the der(9) and der(7) products of t(7;9)(q34;q32), a recurrent translocation of human acute lymphoblastic leukemias (T-ALL). In each of three separate cases, the translocation has divided the TCR-beta locus, juxtaposing chromosome 9 DNA 5' to a J-region in the der(9) product and 3' to a D-region in the der(7) product, with variably sized N-insertions and small deletions detectable at the junctions. All three cases contain breakpoints in chromosome 9 DNA tightly clustered between two closely spaced, and oppositely oriented heptamer sequences, CAC(A/T)GTG, which perfectly match the consensus heptamer sequence recognized by the lymphocyte recombinase apparatus in normal antigen receptor gene rearrangement. In no case was there evidence of directly duplicated sequences in the two reciprocal products, as is often associated with recombination involving random staggered breakage of DNA. Taken together, these results support a mechanism for this particular translocation proceeding by recombinase-mediated breakage of both participating chromosomes.
淋巴肿瘤中的染色体易位通常源于正常重排的抗原受体基因与正常非重排的第二个基因座之间的重组。淋巴细胞重组酶装置在确定第二个基因座的断裂位置中发挥作用的可能性一直存在争议,因为在此位点的断点附近七聚体样识别序列的存在并不一致。为了进一步研究这个问题,对t(7;9)(q34;q32)(人类急性淋巴细胞白血病(T-ALL)的一种常见易位)的der(9)和der(7)产物中的DNA重组位点进行了分析。在三个独立的病例中,每一个病例的易位都将TCR-β基因座分开,使9号染色体DNA在der(9)产物中与一个J区域的5'端并列,在der(7)产物中与一个D区域的3'端并列,在连接处可检测到大小不一的N插入和小缺失。所有三个病例在9号染色体DNA中的断点都紧密聚集在两个紧密间隔且方向相反的七聚体序列CAC(A/T)GTG之间,这与正常抗原受体基因重排中淋巴细胞重组酶装置识别的共有七聚体序列完全匹配。在任何一个病例中,两个相互产物中都没有直接重复序列的证据,而这通常与涉及DNA随机交错断裂的重组相关。综上所述,这些结果支持了一种由重组酶介导参与易位的两条染色体断裂从而导致这种特定易位的机制。