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一例海德综合征:主动脉瓣置换术后病情缓解

A case of Heyde syndrome: resolution following aortic valve replacement.

作者信息

Taguchi Takahiro, Watanabe Masazumi, Watadani Keisuke, Katayama Keijiro, Takahashi Shinya, Takasaki Taiichi, Kurosaki Tatsuya, Imai Katsuhiko, Sueda Taijiro

机构信息

Department of Cardiovascular Surgery, Hiroshima University Hospital, Hiroshima, Japan.

出版信息

Heart Surg Forum. 2014 Oct 1;17(5):E258-60. doi: 10.1532/HSF98.2014370.

DOI:10.1532/HSF98.2014370
PMID:25367238
Abstract

Heyde syndrome is a triad of aortic stenosis, acquired coagulopathy, and anemia due to bleeding from intestinal angiodysplasia. Here we describe a case of this syndrome. An 80-year-old woman with severe aortic stenosis was referred to our department for an aortic valve replacement. She suffered from recurrent iron-deficiency anemia and required transfusions every 2 weeks. Gastroscopy and colonoscopy were normal with the exception of angiodysplasia without bleeding in the cecum. After aortic valve replacement her anemia was resolved. She was discharged on postoperative day 22. No transfusions were needed after the procedure. To date, her hemoglobin has remained stable at >10 mg/dL.

摘要

海德综合征是一种由主动脉瓣狭窄、获得性凝血病以及因肠道血管发育异常出血导致的贫血所组成的三联征。在此我们描述一例该综合征病例。一名患有严重主动脉瓣狭窄的80岁女性因主动脉瓣置换术被转诊至我科。她患有复发性缺铁性贫血,每2周需要输血。胃镜和结肠镜检查均正常,仅在盲肠发现血管发育异常但无出血。主动脉瓣置换术后她的贫血得到缓解。她于术后第22天出院。术后无需输血。迄今为止,她的血红蛋白一直稳定在>10mg/dL。

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A case of Heyde syndrome: resolution following aortic valve replacement.一例海德综合征:主动脉瓣置换术后病情缓解
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引用本文的文献

1
Heyde's syndrome: a systematic review of case reports.海迪综合征:病例报告的系统评价。
BMJ Open Gastroenterol. 2022 May;9(1). doi: 10.1136/bmjgast-2021-000866.
2
Disappearance of Angiodysplasia Following Transcatheter Aortic Valve Implantation in a Patient with Heyde's Syndrome: A Case Report and Review of the Literature.经导管主动脉瓣植入术后 Heyde 综合征患者合并脑动静脉畸形消失:病例报告及文献复习。
J Atheroscler Thromb. 2020 Mar 1;27(3):271-277. doi: 10.5551/jat.49239. Epub 2019 Aug 3.