静观其变：一段长达5年的“复发性痴呆”病史。
Wait and see: a 5 year history of 'recurrent dementia'.
作者信息
D'Angelo Roberto, Rinaldi Rita, Parchi Piero, Cirignotta Fabio
机构信息
Department of UO Neurology, AOU Bologna, S Orsola-Malpighi Hospital, Bologna, Italy.
Department of Biomedical Neuromotor Sciences, University of Bologna, Bologna, Italy.
出版信息
BMJ Case Rep. 2014 Nov 19;2014:bcr2014205991. doi: 10.1136/bcr-2014-205991.
Abstract
Rapid evolving cognitive impairment can be the onset of either a progressive or a treatable dementia. We describe a case of a man in whom the clinical and laboratory presentation suggested a diagnosis of Creutzfeldt-Jakob disease, which subsequently turned into a diagnosis of voltage-gated potassium channel complex antibodies limbic encephalitis. The natural history and an increased knowledge of limbic encephalitis and the related antibodies led us to the correct diagnosis.
摘要
快速进展的认知障碍可能是进行性痴呆或可治疗性痴呆的起始表现。我们描述了一例男性病例，其临床和实验室表现提示为克雅氏病诊断，随后却转变为电压门控钾通道复合物抗体边缘叶脑炎的诊断。边缘叶脑炎及其相关抗体的自然病程和更多认识使我们得出了正确诊断。
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