Di Cesare Ernesto, Di Sibio Alessandra, Lanni Giuseppe, Gennarelli Antonio, Masciocchi Carlo
Department of Radiology, University of L'Aquila, Italy.
J Radiol Case Rep. 2014 May 31;8(5):9-15. doi: 10.3941/jrcr.v8i5.1715. eCollection 2014 May.
Aneurysm of the Membranous Septum (AMS) is a rare cardiac disease, mostly associated with other cardiac anomalies, very rare in the absence of other congenital heart defects. A prompt diagnosis is important, due to severe potential complications, but remain challenging. Most of the cases were earlier diagnosed using ventriculography, but, with the availability of echocardiography and cardiovascular magnetic resonance (CMR), this disease can be accurately assessed non-invasively. We report a case of a 62 years old female patient, without other cardiac congenital disease, who was incidentally diagnosed, by means of CMR with a true and isolated AMS. Our report underlines CMR usefulness in AMS diagnosis, thanks to accurate evaluation (both morphologic and functional) provided by this diagnostic tool, which is able to demonstrate clearly the presence of AMS (aneurysm of the membranous septum) and depict its features.
膜性间隔动脉瘤(AMS)是一种罕见的心脏疾病,大多与其他心脏异常相关,在无其他先天性心脏缺陷的情况下极为罕见。由于存在严重的潜在并发症,及时诊断很重要,但仍具有挑战性。大多数病例早期通过心室造影诊断,但随着超声心动图和心血管磁共振(CMR)的应用,这种疾病可以通过非侵入性方法准确评估。我们报告一例62岁女性患者,无其他心脏先天性疾病,通过CMR偶然诊断为真性孤立性AMS。我们的报告强调了CMR在AMS诊断中的作用,这得益于该诊断工具提供的准确评估(形态学和功能方面),它能够清晰显示AMS(膜性间隔动脉瘤)的存在并描绘其特征。