支气管迪厄拉富瓦病：一例报告并文献复习
Dieulafoy's disease of the bronchus: report of a case and review of the literature.
作者信息
Fang Yu, Wu Qingchen, Wang Bin
机构信息
Department of Thoracic & Cardiovascular Surgery, The First Affiliated Hospital of Chongqing Medical University, 1 Youyi Road, Yuzhong District, 400016, Chongqing, China.
出版信息
J Cardiothorac Surg. 2014 Dec 2;9:191. doi: 10.1186/s13019-014-0191-8.
BACKGROUND
Dieulafoy's disease is a vascular anomaly characterized by the presence of a tortuous dysplastic artery in the submucosa. Although frequently occurring in the gastrointestinal tract, multiple cases of Dieulafoy's disease in the bronchus have been reported in the literature.
METHODS AND RESULTS
We report a case of a 15-year-old boy suffering recurrent massive hemoptysis. Bilobectomy stopped bleeding after unsuccessful treatment with embolization of bronchial artery.
CONCLUSION
It is concluded a congenital origin of this disease. Angiography and endobronchial ultrasonography can be used to diagnose Dieulafoy's disease of bronchus whereas bronchoscopy biopsy should be avoided. Surgery is needed when embolization fails.
背景
Dieulafoy病是一种血管异常疾病，其特征是黏膜下层存在一条迂曲发育异常的动脉。尽管Dieulafoy病常发生于胃肠道，但文献中已报道了多例支气管Dieulafoy病。
方法与结果
我们报告了一例15岁反复大量咯血的男孩。在支气管动脉栓塞治疗失败后，肺叶切除术止住了出血。
结论
得出该病起源于先天性的结论。血管造影和支气管内超声可用于诊断支气管Dieulafoy病，而应避免进行支气管镜活检。栓塞失败时需要进行手术。
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