Hasan Ashfaq, Sastry B K S, Aleem M A, Reddy Gokul, Mahmood Syed
Professor and Head, Department of Pulmonary Medicine, Deccan College of Medical Sciences/Owaisi Hospital, Hyderabad, India; Consultant Pulmonologist, Care Institute of Medical Sciences (Banjara), Hyderabad, India.
Consultant Cardiologist, Care Institute of Medical Sciences (Nampally), Hyderabad, India.
Indian Heart J. 2014 Sep-Oct;66(5):535-8. doi: 10.1016/j.ihj.2014.09.001. Epub 2014 Sep 24.
Idiopathic Pulmonary Hypertension (IPAH) is characterized by elevated pulmonary arterial pressure in the absence of an identifiable underlying cause. The condition is usually relentlessly progressive with a short survival in the absence of treatment.(1) We describe a patient of IPAH in whom the pulmonary artery pressures significantly abated with complete disappearance of symptoms, following spontaneous development of a pulmonary arterio-venous malformation (PAVM).
特发性肺动脉高压(IPAH)的特征是在没有可识别的潜在病因的情况下肺动脉压力升高。在没有治疗的情况下,这种疾病通常会持续进展,生存期较短。(1)我们描述了一名特发性肺动脉高压患者,该患者在自发形成肺动静脉畸形(PAVM)后,肺动脉压力显著降低,症状完全消失。