Nomani Ali Zohair, Toori Kaleem Ullah
Department of Medicine, KRL Hospital, Islamabad.
J Coll Physicians Surg Pak. 2014 Dec;24(12):949-51.
Bronchopulmonary sequestration is a rare congenital malformation of the lower respiratory tract comprising of a nonfunctioning lung tissue mass that lacks normal communication with the tracheobronchial tree. The diagnosis may be easily missed as many of the symptoms of bronchopulmonary sequestration overlap with that of other pulmonary diseases. Bronchopulmonary sequestration can be complicated by recurrent infections, hemorrhage and malignant transformation and, therefore, needs to be timely diagnosed and resected to decrease both morbidity and mortality. A high degree of suspicion in the differential diagnosis helps diagnose the positive cases. The parenchymal abnormalities associated with bronchopulmonary sequestration are best visualized using computed tomography, although their appearance is variable. We report the case of a 14 years old boy with intralobar bronchopulmonary sequestration with the sole manifestation of recurrent pneumonias.
支气管肺隔离症是一种罕见的下呼吸道先天性畸形，由无功能的肺组织团块组成，该组织团块与气管支气管树缺乏正常连通。由于支气管肺隔离症的许多症状与其他肺部疾病的症状重叠，其诊断可能很容易被漏诊。支气管肺隔离症可并发反复感染、出血和恶变，因此需要及时诊断并切除，以降低发病率和死亡率。在鉴别诊断中保持高度怀疑有助于诊断出阳性病例。尽管支气管肺隔离症相关的实质异常表现多样，但使用计算机断层扫描能最好地显示这些异常。我们报告一例14岁患有叶内型支气管肺隔离症的男孩，其唯一表现为反复肺炎。
