Öztürk Murat, Erdoğan Selvet, Kara Ahmet, Sarı Fatih
Department of Otolaryngology, Medical Faculty of Kocaeli University, 41380 Umuttepe, Kocaeli, Turkey.
Kulak Burun Bogaz Ihtis Derg. 2014 Nov-Dec;24(6):361-3. doi: 10.5606/kbbihtisas.2014.75983.
Angiokeratomas are benign mucocutaneous lesions which are composed of enlarged veins in the dermis of the skin. Although angiokeratomas may be part of a systemic disease, it is important to distinguish them from other vascular lesions. In this report, we present a rare case of angiokeratoma of the nasal vestibule. To our knowledge, this is the first nasal angiokeratoma case in the literature. The diagnostic and treatment features of this case and the association of angiokeratoma with systemic diseases like Fabry disease were discussed.
血管角皮瘤是一种良性黏膜皮肤病变，由皮肤真皮层中扩张的静脉组成。尽管血管角皮瘤可能是一种全身性疾病的一部分，但将它们与其他血管病变区分开来很重要。在本报告中，我们呈现了一例罕见的鼻前庭血管角皮瘤病例。据我们所知，这是文献中首例鼻血管角皮瘤病例。本文讨论了该病例的诊断和治疗特点以及血管角皮瘤与法布里病等全身性疾病的关联。
