Cuch Barbara, Opasała Urszula, Nachulewicz Paweł, Szumiło Justyna
Department of Paediatric Surgery and Traumatology, Medical University of Lublin, Lublin, Poland.
Department of Clinical Pathomorphology, Medical University of Lublin, Lublin, Poland.
Wideochir Inne Tech Maloinwazyjne. 2014 Dec;9(4):658-61. doi: 10.5114/wiitm.2014.45885. Epub 2014 Oct 9.
Inflammatory myofibroblastic tumour is an uncommon tumour of intermediate malignant potential. Its aetiology is still unclear. It occurs predominantly in children and young adults. This report presents a case of pulmonary inflammatory myofibroblastic tumour in a 5-year-old girl. The patient had a history of recurrent respiratory tract infections. A chest radiograph and computed tomography chest scan showed a round mass in the lower lobe of her left lung. Thoracoscopic marginal excision of the tumour with an Endo-GIA stapler device (TYCO healthcare) was performed. Histological examination confirmed the final diagnosis of inflammatory myofibroblastic tumour. Postoperative recovery was uncomplicated and the patient was discharged 6 days after surgery. Round masses located in the lungs are very rare in children and the possibility of myofibroblastic tumour as well as metastatic lesions should be taken into consideration in such cases. Thoracoscopic excision is the best option in distally located lesions.
炎性肌纤维母细胞瘤是一种具有中等恶性潜能的罕见肿瘤。其病因仍不清楚。它主要发生于儿童和年轻人。本报告介绍了一名5岁女孩患肺炎性肌纤维母细胞瘤的病例。该患者有反复呼吸道感染病史。胸部X线片和胸部计算机断层扫描显示其左肺下叶有一个圆形肿块。使用Endo-GIA吻合器装置（泰科医疗）对肿瘤进行了胸腔镜边缘切除。组织学检查确诊为炎性肌纤维母细胞瘤。术后恢复顺利，患者术后6天出院。儿童肺部出现圆形肿块非常罕见，在这种情况下应考虑肌纤维母细胞瘤以及转移性病变的可能性。胸腔镜切除是位于远端病变的最佳选择。
