Khoder Wael Y, Stief Christian G, Burgmann Maximiliane, Burges Alexander
Department of Urology, University Hospital Munich-Grosshadern, Ludwig-Maximilians-University Munich, Marchioninistrasse 15, 81377, Munich, Germany,
Int Urogynecol J. 2015 Jul;26(7):1083-7. doi: 10.1007/s00192-014-2609-1. Epub 2015 Jan 15.
Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) is a rare genital aplasia syndrome. Patients with MRKH regularly dilate their neovagina with vaginal dilatators.
A 23-year-old MRKH syndrome patient came to our department complaining of a lost vaginal dilator, which she had inserted 2 days previously. She had no bleeding or abdominal pain, but did have occasional urine loss. She had a history of abdominal exploration for an acute abdomen and the creation of a neovagina at the age of 16. An abdominal CT scan located the dislocated dilator intravesically. After diagnostic laparoscopy, the dilator was removed through the vesico-neovaginal perforation. The vagina was closed and covered by a pedicled peritoneal flap, followed by closure of the urinary bladder. An omental J-flap was then fixed between the vagina and bladder.
The operative time was 185 min, with no significant blood loss, injuries or need for conversion/revision. The indwelling catheter was removed 7 days later after cystography, followed by normal micturition and an adequate bladder capacity. Vaginal dilation and sexual activity was resumed 1 month postoperatively. Follow-up was uneventful.
Laparoscopic vaginal dilator removal with immediate repair of the perforation of the neovagina and the urinary bladder directly after an acute trauma in a patient with MRKH syndrome may be a management option. It is a feasible, safe and viable operation in the hands of experienced laparoscopists.
迈耶-罗基坦斯基-库斯特-豪泽综合征(MRKH)是一种罕见的生殖器发育不全综合征。患有MRKH的患者经常使用阴道扩张器扩张其新阴道。
一名23岁的MRKH综合征患者前来我科就诊,主诉2天前插入的阴道扩张器丢失。她没有出血或腹痛,但偶尔会出现尿失禁。她有因急腹症进行腹部探查以及16岁时创建新阴道的病史。腹部CT扫描显示移位的扩张器位于膀胱内。诊断性腹腔镜检查后,通过膀胱-新阴道穿孔取出扩张器。关闭阴道并用带蒂腹膜瓣覆盖,随后关闭膀胱。然后将网膜J形瓣固定在阴道和膀胱之间。
手术时间为185分钟,无明显失血、损伤,无需中转/修正。膀胱造影后7天拔除留置导尿管,随后排尿正常,膀胱容量充足。术后1个月恢复阴道扩张和性活动。随访情况良好。
对于MRKH综合征患者在急性创伤后立即进行腹腔镜下阴道扩张器取出并直接修复新阴道和膀胱穿孔可能是一种治疗选择。在经验丰富的腹腔镜手术医生手中,这是一种可行、安全且有效的手术。