Taurino Maurizio, Ficarelli Roberta, Rizzo Luigi, Stella Nazzareno, Persiani Francesca, Capuano Fabio
Vascular Surgery Department, University of Rome" La Sapienza", Sant' Andrea Hospital, Rome, Italy.
Vascular Surgery Department, University of Rome" La Sapienza", Sant' Andrea Hospital, Rome, Italy.
Ann Vasc Surg. 2015 Apr;29(3):595.e5-9. doi: 10.1016/j.avsg.2014.10.034. Epub 2015 Jan 14.
Marfan syndrome is a heritable disorder of connective tissue leading to aortic aneurysms and other cardiovascular complications associated with reduced life expectancy. Although contemporary management of ascending aortic disease requires open surgical reconstruction, the combined retrograde visceral revascularization and endovascular exclusion (hybrid procedure) of entire thoracoabdominal aorta has been introduced for the management of descending thoracic and abdominal aortic pathology. The present experience reports 2 cases of thoracoabdominal aortic aneurysms, in Marfan patients, previously submitted to major cardiovascular surgical procedures, through a hybrid approach.
马凡综合征是一种结缔组织遗传性疾病，可导致主动脉瘤及其他心血管并发症，进而缩短预期寿命。尽管目前升主动脉疾病的治疗需要进行开放性手术重建，但对于降胸主动脉和腹主动脉病变的治疗，已引入了联合逆行内脏血管重建术和血管腔内隔绝术（杂交手术）。本文报告了2例马凡综合征患者的胸腹主动脉瘤病例，此前这些患者已通过杂交手术方法接受了重大心血管外科手术。
