Cade Jacqueline, Jansen Nicholas
From the Department of Anesthesia, Royal Melbourne Hospital, Victoria, Australia.
A A Case Rep. 2014 Jun 15;2(12):152-4. doi: 10.1213/XAA.0000000000000031.
The mucopolysaccharidoses are a group of lysosomal storage diseases with many skeletal and airway features that pose a challenge to anesthetists. We present the anesthetic management of a woman with mucopolysaccharidosis type VI undergoing cervical spine surgery and review the perioperative issues that may arise with this disease.
黏多糖贮积症是一组溶酶体贮积病,具有许多骨骼和气道特征,给麻醉医生带来了挑战。我们介绍了一名患有VI型黏多糖贮积症的女性患者接受颈椎手术的麻醉管理,并回顾了该疾病可能出现的围手术期问题。