Park J H, Kim S H, Kim H J, Lee S J, Jeong D C, Kim S Y
Department of Pediatrics, College of Medicine, The Catholic University of Korea, Yeouido St. Mary's Hospital, Seoul, Republic of Korea.
J Perinatol. 2015 Feb;35(2):158-60. doi: 10.1038/jp.2014.207.
Macrophage activation syndrome (MAS) is a complication of rheumatic disorders characterized by cytopenia, multiple organ dysfunction and coagulopathy associated with an inappropriate activation of macrophage. In neonatal lupus erythematosus, MAS is rare but fatal, requiring early diagnosis and treatment for optimal outcome. We report a case of MAS in a neonate born to a mother with autoimmune disease, improved by treatment with steroid, intravenous immunoglobulin and cyclosporine.
巨噬细胞活化综合征(MAS)是一种风湿性疾病的并发症,其特征为血细胞减少、多器官功能障碍和凝血病,与巨噬细胞的不适当活化有关。在新生儿红斑狼疮中,MAS罕见但可致命,需要早期诊断和治疗以获得最佳预后。我们报告一例患有自身免疫性疾病的母亲所生新生儿发生MAS的病例,经类固醇、静脉注射免疫球蛋白和环孢素治疗后病情改善。