Nazari Ferdos, Azimi Amirreza, Abdi Siamak
Department of Neurology, School of Medicine, Shariati Hospital, Tehran University of Medical Sciences, Tehran, Iran.
Department of Neurology, School of Medicine, Sina Hospital, Tehran University of Medical Sciences, Tehran, Iran.
Iran J Neurol. 2014 Oct 6;13(4):209-14.
Susac's syndrome (SS) is a clinical triad of encephalopathy, branch retinal artery occlusion and sensorineural hearing loss and maybe due to an immune-mediated endotheliopathy. Because of its rarity and some similarities to other common neurological conditions such as multiple sclerosis and acute disseminated encephalomyelitis, it is often misdiagnosed and therefore mistreated. To the best of our knowledge, there is only one case report from our country with this diagnosis. Here, we have a short discussion on this issue to introduce it to our colleagues and remind it as a differential diagnosis in patients with unexplained encephalopathy.
Susac综合征(SS)是一种具有脑病、视网膜分支动脉阻塞和感音神经性听力损失的临床三联征,可能由免疫介导的内皮病变引起。由于其罕见性以及与其他常见神经系统疾病(如多发性硬化症和急性播散性脑脊髓炎)存在一些相似之处,它常被误诊,进而得到不当治疗。据我们所知,我国仅有一例关于此诊断的病例报告。在此,我们就这个问题进行简短讨论,以便向我们的同行介绍它,并提醒在患有不明原因脑病的患者中应将其作为鉴别诊断。