Tomimatsu Takuji, Sugihara Mika, Nakamura Takafumi, Kashihara Naoki, Shimoya Koichiro
Department of Obstetrics and Gynecology, Kawasaki Medical School, Kurashiki, Japan.
Gynecol Obstet Invest. 2015;79(3):168-71. doi: 10.1159/000369996. Epub 2015 Feb 3.
A uterine cyst occurring as an extrarenal manifestation of autosomal dominant polycystic kidney disease (ADPKD) is extremely rare.
A 46-year-old Japanese woman was referred with a large abdominal mass causing severe abdominal distension. A large uterine cyst as an extrarenal manifestation of ADPKD was strongly suspected. First, we managed this patient by aspirating the cyst fluid through a small laparotomy. A year later, the cyst recurred and the patient underwent hysterectomy. Massive cystic degeneration of a uterine leiomyoma was diagnosed histologically.
We described the rare case of massive cystic degeneration of a uterine leiomyoma in a patient with ADPKD, in which a causal relationship was suspected.
作为常染色体显性多囊肾病（ADPKD）肾外表现的子宫囊肿极为罕见。
一名46岁的日本女性因巨大腹部肿块导致严重腹胀前来就诊。强烈怀疑是作为ADPKD肾外表现的巨大子宫囊肿。首先，我们通过小切口剖腹术抽吸囊液对该患者进行治疗。一年后，囊肿复发，患者接受了子宫切除术。组织学诊断为子宫平滑肌瘤的大量囊性变。
我们描述了一例ADPKD患者子宫平滑肌瘤大量囊性变的罕见病例，怀疑二者存在因果关系。
