Rajadhyaksha Anjali, Sonawale Archana, Agrawal Ajay, Ahire Kiran, Kawale Juhi
J Assoc Physicians India. 2014 Jul;62(7):637-41.
Hemophagocytic lymphohistiocytosis (HLH), is an uncommon, life-threatening hyperinflammatory syndrome caused by severe hypercytokinemia with excessive activation of lymphocytes and macrophages due to a highly stimulated but ineffective immune process. We report a case of Hemophagocytic Lymphohistiocytosis in a 15 year old boy presenting with fever, lymphadenopathy and pancytopenia due to infection caused by Klebsiella Pneumoniae and Acinetobacter.
噬血细胞性淋巴组织细胞增生症(HLH)是一种罕见的、危及生命的高炎症综合征,由严重的高细胞因子血症引起,由于免疫过程受到高度刺激但无效,导致淋巴细胞和巨噬细胞过度活化。我们报告一例15岁男孩的噬血细胞性淋巴组织细胞增生症,该男孩因肺炎克雷伯菌和不动杆菌感染出现发热、淋巴结病和全血细胞减少。