Ozeren Ersin, Gurses Levent, Sorar Mehmet, Er Uygur, Önder Evrim, Arıkök Ata Türker
Department of Neurosurgery, Diskapi Training and Research Hospital, Duzce, Turkey.
Department of Neurosurgery, Medical School, Duzce University, Duzce, Turkey.
Asian J Neurosurg. 2014 Oct-Dec;9(4):246. doi: 10.4103/1793-5482.146666.
L'hermitte-Duclos disease (LDD) is an extremely rare cerebellar lesion of uncertain etiology. Occasionally, the patients with LDD may even have sudden neurological deterioration due to acute heniation as seen in the present case report. It is also imperative to distinguish this disease from other malignant lesion of the cerebellum and cerebellar malformations with its varied natural course of history and hence better ability to prognosticate such patients. Herein, we reported a successfully treated case of LDD following a long history of vaguely defined neurological complaints in an elderly patient and reviewed the literature.
赫米特-迪克洛病（LDD）是一种病因不明的极为罕见的小脑病变。偶尔，LDD患者甚至可能因急性疝出而出现突然的神经功能恶化，如本病例报告所示。鉴于其多样的自然病程以及因此对这类患者更好的预后判断能力，将这种疾病与其他小脑恶性病变和小脑畸形区分开来也至关重要。在此，我们报告了一例老年患者在长期存在不明神经症状后成功治疗的LDD病例，并对相关文献进行了综述。
