成人先天性胆脂瘤的非典型表现及良好听力结果的病例
Atypical presentation of congenital cholesteatoma in an adult case with good hearing result.
作者信息
Solmaz Fevzi, Akduman Davut, Haksever Mehmet, Gündoğdu Ercan, Mescioğlu Atilla
机构信息
Bursa Sevket Yilmaz Training and Research Hospital, Department of Otorhinolaryngology, 16800 Yıldırım, Bursa, Turkey.
出版信息
Ann Med Surg (Lond). 2015 Jan 17;4(1):26-9. doi: 10.1016/j.amsu.2015.01.001. eCollection 2015 Mar.
INTRODUCTION
Congenital cholesteatoma is thought to be caused by inadequate folding of the epidermoid formation inside the middle ear cleft. During development of the middle ear mucosa, stratified squamous epithelium accumulates in the embryonic life. Its typical appearance is a "pearl" beneath the anterosuperior quadrant of the tympanic membrane.
PRESENTATION OF CASE
We report 28 years-old case with congenital cholesteatoma in the posterosuperior quadrant of middle ear cavity. The main complaint was the hearing loss which had developed slowly over several years.
DISCUSSION
The case was surgically treated. Postoperative hearing result was satisfactory.
CONCLUSION
Congenital cholesteatoma may occur in atypical locations and ages. Many authors prefer canal wall down tympanomastoidectomy. But it can also be treated successfully by intact canal wall tympanomastoidectomy with good hearing results.
引言
先天性胆脂瘤被认为是由中耳裂内表皮样结构折叠不充分所致。在中耳黏膜发育过程中，分层鳞状上皮在胚胎期积聚。其典型表现为鼓膜前上象限下方的“珍珠”。
病例介绍
我们报告一例28岁患者，中耳腔后上象限存在先天性胆脂瘤。主要症状是听力损失，已持续数年且呈缓慢进展。
讨论
该病例接受了手术治疗。术后听力结果令人满意。
结论
先天性胆脂瘤可能发生在非典型部位和年龄段。许多作者更倾向于开放式鼓室乳突切除术。但完整外耳道壁鼓室乳突切除术也可成功治疗，且听力效果良好。
Zotero 插件