Wallett Arabella, Ibbetson Jan S, Kearney Daniel, Newland Kate, Sidhu Shireen
Royal Adelaide Hospital, Adelaide, South Australia, Australia.
Pathology SA, Adelaide, South Australia, Australia.
Australas J Dermatol. 2015 Aug;56(3):197-201. doi: 10.1111/ajd.12307. Epub 2015 Mar 6.
Peripheral T-cell lymphoma, not otherwise specified (PTCL, NOS) is a rare, heterogeneous group of nodal and extranodal mature T-cell lymphomas that do not correspond to any of the defined T-cell entities, according to the World Health Organization classification. Most cases present with late stage nodal disease; however extranodal involvement is common. Skin and subcutaneous involvement is reported in approximately 20% of cases. Little attention has been given to the highly variable skin manifestations in the literature. It is our experience that lesions can present in ways other than previously described nodular or tumourous lesions that often ulcerate. We present a case series from a large tertiary institution of seven cases of PTCL, NOS with skin involvement, highlighting the variable presentations and diagnostic challenges for this heterogeneous group.
外周T细胞淋巴瘤,非特指型(PTCL,NOS)是一种罕见的、异质性的淋巴结和结外成熟T细胞淋巴瘤,根据世界卫生组织分类,它不符合任何已定义的T细胞实体。大多数病例表现为晚期淋巴结疾病;然而,结外受累很常见。约20%的病例报告有皮肤和皮下受累。文献中对高度可变的皮肤表现关注较少。我们的经验是,病变的表现方式可能不同于先前描述的通常会溃疡的结节状或肿瘤性病变。我们展示了一家大型三级医疗机构的7例PTCL,NOS皮肤受累病例系列,突出了这一异质性群体的可变表现和诊断挑战。