与卡塔格内综合征相关的右侧博赫达勒克疝：发育及临床观察

Right bochdalek hernia associated with kartagener syndrome: developmental and clinical observations.

作者信息

Romeo Carmelo, Turiaco Nunzio, Gitto Eloisa, Borruto Francesca Astra, Santoro Giuseppe

机构信息

Department of Pediatrics, Gynecology, Microbiology, and Biomedical Sciences, Policlinico G. Martino, University of Messina, Messina, Italy.

Department of Biomorphology and Biotechnologies, Policlinico G. Martino, University of Messina, Messina, Italy.

出版信息

European J Pediatr Surg Rep. 2013 Jun;1(1):15-7. doi: 10.1055/s-0033-1343077. Epub 2013 Apr 15.

DOI:10.1055/s-0033-1343077

PMID:25755941

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4336051/

Abstract

We present a novel case of the association of right-sided Bochdalek hernia, a diaphragmatic life-threatening malformation, and Kartagener syndrome, which is characterized by congenital bronchiectasis, chronic sinusitis, and situs inversus. The developmental and clinical findings are discussed. When an association of diaphragmatic hernia with situs viscerum inversus is encountered, physicians should be mindful of the possibility of Kartagener syndrome because this condition could significantly affect the morbidity of the patient.

摘要

我们报告了一例罕见病例，该病例为右侧Bochdalek疝（一种危及生命的膈肌畸形）与Kartagener综合征相关联，后者的特征为先天性支气管扩张、慢性鼻窦炎和内脏转位。文中讨论了其发育和临床发现。当遇到膈肌疝合并内脏转位的情况时，医生应留意Kartagener综合征的可能性，因为这种病症可能会显著影响患者的发病率。